2021第五版中枢神经系统肿瘤分类（斜体为临时分类）
胶质瘤，胶质细胞瘤和神经细胞瘤
Gliomas, glioneuronal tumors, and neuronal tumors
成人型型弥漫性胶质瘤
Adult-type diffuse gliomas
星形细胞瘤，IDH突变
Astrocytoma, IDH-mutant
少突胶质细胞瘤，IDH突变和1p/19q缺失
Oligodendroglioma, IDH-mutant, and 1p/19q-codeleted
胶质母细胞瘤，IDH野生型
Glioblastoma, IDH-wildtype
儿童型弥漫性低级别胶质瘤
Pediatric-type diffuse low-grade gliomas
弥漫性星形细胞瘤，MYB或MYB1变异
Diffuse astrocytoma, MYB- or MYBL1-altered
血管中心性胶质瘤
Angiocentric glioma
青年多形态低级别神经上皮肿瘤
Polymorphous low-grade neuroepithelial tumor of the young
弥漫低级别胶质瘤，MAPK通路改变
Diffuse low-grade glioma, MAPK pathway-altered
儿童型弥漫性高级别胶质瘤
Pediatric-type diffuse high-grade gliomas
弥漫中线胶质瘤，H3 k27改变
Diffuse midline glioma, H3 K27-altered
弥漫半球胶质瘤，H3 G34 突变
Diffuse hemispheric glioma, H3 G34-mutant
弥漫儿型高级别胶质瘤，H3-野生型和IDH -野生型
Diffuse pediatric-type high-grade glioma, H3-wildtype and IDH-wildtype
婴儿型半球胶质瘤
Infant-type hemispheric glioma
局限性星形细胞胶质瘤
Circumscribed astrocytic gliomas
毛细胞性星形细胞胶质瘤
Pilocytic astrocytoma
高级别星形细胞胶质瘤，具有卵泡样特征
High-grade astrocytoma with piloid features
多形性黄色星形细胞瘤
Pleomorphic xanthoastrocytoma
室管膜下巨细胞星形细胞瘤
Subependymal giant cell astrocytoma
脊索样胶质瘤
Chordoid glioma
星形细胞瘤，MN1改变
Astroblastoma, MN1-altered
胶质神经元混合和神经元肿瘤
Glioneuronal and neuronal tumors
神经节胶质瘤
Ganglioglioma
促结缔组织增生性婴儿神经节胶质瘤/促结缔组织增生性婴儿星形细胞瘤
Desmoplastic infantile ganglioglioma / desmoplastic infantile astrocytoma
胚胎发育不良性神经上皮肿瘤
Dysembryoplastic neuroepithelial tumor
弥漫性胶质神经元瘤，具有少突胶质细胞样特征和簇状核
Diffuse glioneuronal tumor with oligodendroglioma-like features and nuclear clusters
乳头状胶质神经元瘤
Papillary glioneuronal tumor
菊型团形成性胶质神经元瘤
Rosette-forming glioneuronal tumor
黏液样胶质细胞瘤
Myxoid glioneuronal tumor
弥漫性软脑膜胶质神经元瘤
Diffuse leptomeningeal glioneuronal tumor
节细胞瘤
Gangliocytoma
多结节性和空泡性神经元瘤
Multinodular and vacuolating neuronal tumor
发育不良的小脑神经节细胞瘤(lhermitt - duclos病)
Dysplastic cerebellar gangliocytoma (Lhermitte-Duclos disease)
中枢神经细胞瘤
Central neurocytoma
脑室外神经细胞瘤
Extraventricular neurocytoma
小脑脂肪神经细胞瘤
Cerebellar liponeurocytoma
室管膜瘤
Ependymal tumors
幕上室管膜
Supratentorial ependymoma
幕上室管膜瘤，ZFTA融合阳性
Supratentorial ependymoma, ZFTA fusion-positive
幕上室管膜瘤，YAP1融合阳性
Supratentorial ependymoma, YAP1 fusion-positive
颅后窝室管膜瘤
Posterior fossa ependymoma
颅后窝室管膜瘤，PFA组
Posterior fossa ependymoma, group PFA
颅后窝室管膜瘤，PFB组
Posterior fossa ependymoma, group PFB
脊髓室管膜瘤
Spinal ependymoma
脊髓室管膜瘤，MYCN扩增
Spinal ependymoma, MYCN-amplified
黏液乳头状室管膜瘤
Myxopapillary ependymoma
室管膜下室管膜瘤
Subependymoma
脉络膜丛肿瘤
Choroid plexus tumors
脉络膜丛乳头状瘤
Choroid plexus papilloma
非典型脉络膜丛乳头状瘤
Atypical choroid plexus papilloma
脉络膜丛癌
Choroid plexus carcinoma
胚胎性肿瘤
Embryonal tumors
髓母细胞瘤
Medulloblastoma
分子定义的髓母细胞瘤
Medulloblastomas, molecularly defined
髓母细胞瘤，WNT激活型
Medulloblastoma, WNT-activated
髓母细胞瘤，SHH激活的和tp53 -野型
Medulloblastoma, SHH-activated and TP53-wildtype
髓母细胞瘤，SHH激活和tp53 突变型
Medulloblastoma, SHH-activated and TP53-mutant
髓母细胞瘤，非WNT /非SHH
Medulloblastoma, non-WNT/non-SHH
组织学定义髓母细胞瘤
Medulloblastomas, histologically defined
其他CNS胚胎性肿瘤
Other CNS embryonal tumors
非典型畸胎样/横纹肌样肿瘤
Atypical teratoid/rhabdoid tumor
筛状神经上皮性肿瘤
Cribriform neuroepithelial tumor
胚胎性肿瘤伴多层菊型团
Embryonal tumor with multilayered rosettes
CNS肿瘤，FOXR2激活型
CNS neuroblastoma, FOXR2-activated
中枢神经肿瘤BCOR内串复制
CNS tumor with BCOR internal tandem duplication
CNS胚胎性肿瘤
CNS embryonal tumor
松果体肿瘤
Pineal tumors
松果体细胞瘤
Pineocytoma
中分化松果体实质肿瘤
Pineal parenchymal tumor of intermediate differentiation
松果体母细胞瘤
Pineoblastoma
松果体区乳头状瘤
Papillary tumor of the pineal region
松果体区促结缔组织增生性黏液样肿瘤，SMARCB1突变
Desmoplastic myxoid tumor of the pineal region, SMARCB1-mutant
颅内及脊旁神经肿瘤
Cranial and paraspinal nerve tumors
神经鞘瘤
Schwannoma
神经纤维瘤
Neurofibroma
神经束膜瘤
Perineurioma
混合神经鞘瘤
Hybrid nerve sheath tumor
恶性黑素性神经鞘瘤
Malignant melanotic nerve sheath tumor
恶性周围神经鞘瘤
Malignant peripheral nerve sheath tumor
副神经节瘤
Paraganglioma
脑膜瘤
Meningiomas
脑膜瘤
Meningioma
非脑膜瘤间叶性肿瘤
Mesenchymal, non-meningothelial tumors
软组织肿瘤
Soft tissue tumors
纤维母细胞和肌纤维母细胞瘤
Fibroblastic and myofibroblastic tumors
孤立性纤维性肿瘤
Solitary fibrous tumor
血管瘤
Vascular tumors
血管瘤和血管畸形
Hemangiomas and vascular malformations
血管母细胞瘤
Hemangioblastoma
骨骼肌肿瘤
Skeletal muscle tumors
横纹肌肉瘤
Rhabdomyosarcoma
分化不确定
Uncertain differentiation
颅内间叶性肿瘤，FET-CREB融合阳性
Intracranial mesenchymal tumor, FET-CREB fusion-positive
CIC重排肉瘤
CIC-rearranged sarcoma
原发性颅内肉瘤，DICER1突变
Primary intracranial sarcoma, DICER1-mutant
Ewing肉瘤
Ewing sarcoma
软骨-骨肿瘤
Chondro-osseous tumors
软骨源性肿瘤
Chondrogenic tumors
间叶性软骨肉瘤
Mesenchymal chondrosarcoma
软骨肉瘤
Chondrosarcoma
脊索肿瘤
Notochordal tumors
脊索瘤(包括低分化脊索瘤)
Chordoma (including poorly differentiated chordoma)
黑素细胞瘤
Melanocytic tumors
弥漫性脑膜黑素细胞肿瘤
Diffuse meningeal melanocytic neoplasms
脑膜黑素细胞增生症和脑膜黑素细胞瘤病
Meningeal melanocytosis and meningeal melanomatosis
局限脑膜黑素细胞瘤
Circumscribed meningeal melanocytic neoplasms
脑膜黑素细胞瘤和脑膜黑色素瘤
Meningeal melanocytoma and meningeal melanoma
淋巴造血肿瘤
Hematolymphoid tumors
淋巴瘤
Lymphomas
CNS淋巴瘤
CNS lymphomas
CNS原发性弥漫性大B细胞淋巴瘤
Primary diffuse large B-cell lymphoma of the CNS
免疫缺陷相关的CNS淋巴瘤
Immunodeficiency-associated CNS lymphoma
淋巴瘤肉芽肿
Lymphomatoid granulomatosis
血管内大B细胞淋巴瘤
Intravascular large B-cell lymphoma
其它少见CNS淋巴瘤
Miscellaneous rare lymphomas in the CNS
硬脑膜MALT淋巴瘤
MALT Iymphoma of the dura
其他低级别B细胞淋巴瘤
Other low-grade B-cell lymphomas of the CNS
间变性大细胞淋巴瘤(ALK+/ALK-)
Anaplastic large cell lymphoma (ALK+/ALK-)
T细胞和NK/T细胞淋巴瘤
T-cell and NK/T-cell lymphomas
组织细胞性肿瘤
Histiocytic tumors
erdheim - chester病
Erdheim-Chester disease
Rosai - Dorfman病
Rosai-Dorfman disease
幼年性黄色肉芽肿
Juvenile xanthogranuloma
朗格汉斯细胞组织细胞增生症
Langerhans cell histiocytosis
组织细胞肉瘤
Histiocytic sarcoma
生殖细胞肿瘤
Germ cell tumors
成熟畸胎瘤
Mature teratoma
不成熟畸胎瘤
Immature teratoma
畸胎瘤伴恶性体细胞肿瘤
Teratoma with somatic-type malignancy
生殖细胞瘤
Germinoma
胚胎癌
Embryonal carcinoma
卵囊瘤
Yolk sac tumor
绒毛膜癌
Choriocarcinoma
混合生殖细胞瘤
Mixed germ cell tumor
鞍区肿瘤
Tumors of the sellar region
造釉细胞性颅咽管瘤
Adamantinomatous craniopharyngioma
乳头状颅咽管瘤
Papillary craniopharyngioma
垂体细胞瘤、鞍区颗粒细胞瘤、梭形细胞嗜酸细胞瘤
Pituicytoma, granular cell tumor of the sellar region, and spindle cell oncocytoma
垂体腺瘤/垂体神经内分泌瘤
Pituitary adenoma/PitNET
垂体母细胞瘤
Pituitary blastoma
中枢神经系统转移癌
Metastases to the CNS
脑和脊髓转移癌
Metastases to the brain and spinal cord parenchyma
脑膜转移癌
Metastases to the meninges
