2020年第五版WHO软组织肿瘤分类
脂肪细胞肿瘤(Adipocytic tumours)
良性(Benign)
8850/0 脂肪瘤 NOS (Lipoma NOS)
8856/0肌内脂肪瘤(Intramuscular lipoma)
软骨样脂肪瘤(Chondroid lipoma)
脂肪瘤病(Lipomatosis)
弥漫性脂肪瘤病(Diffuse lipomatosis)
多发对称性脂肪瘤病(Multiple symmetrical lipomatosis)
盆腔脂肪瘤病(Pelvic lipomatosis)
类固醇脂肪瘤病 (Steroid lipomatosis)
艾滋病毒脂肪代谢障碍 (HIV lipodystrophy)
神经脂肪瘤病 (Lipomatosis of nerve)
8881/0 脂肪母细胞瘤病 (Lipoblastomatosis)
局限性(脂肪母细胞瘤) (Localized (lipoblastoma))
弥漫性(脂肪母细胞瘤病) (Diffuse (lipoblastomatosis))
8861/0 血管脂肪瘤NOS (Angiolipoma NOS)
细胞性血管脂肪瘤 (Cellular angiolipoma)
8890/0 肌脂肪瘤(Myolipoma)
8862/0 软骨样脂肪瘤 (Chondroid lipoma)
8857/0 梭形细胞脂肪瘤(Spindle cell lipoma)
8857/0 非典型梭形细胞/多形性脂肪瘤样肿瘤
(Atypical spindle cell/pleomorphic lipomatous tumour)
8880/0冬眠(Hibernoma）
中间性(局部侵袭性)Intermediate (locally aggressive)
8850/1 非典型性脂肪瘤性肿瘤( Atypical lipomatous tumour)
恶性(Malignant)
8851/3 脂肪肉瘤,高分化, NOS (Liposarcoma, well-differentiated, NOS)
8851/3 脂瘤样脂肪肉瘤(Lipoma-like liposarcoma)
8851/3 炎性脂肪肉瘤(Inflammatory liposarcoma)
8851/3 硬化化性脂肪肉瘤(Sclerosing liposarcoma)
8858/3 去分化脂肪肉瘤(Dedifferentiated liposarcoma)
8852/3黏液样脂肪肉瘤(Myxoid liposarcoma)
8854/3 多形性脂肪肉瘤(Pleomorphic liposarcoma)
上皮样脂肪肉瘤(Epithelioid liposarcoma)
8859/3 粘液样多形性脂肪肉瘤(Myxoid pleomorphic liposarcoma)
成纤维细胞/肌成纤维细胞性肿瘤(Fibroblastic and myofibroblastic tumours)
良性(Benign)
8828/0结节性筋膜炎(Nodular fasciitis)
血管内筋膜炎(Intravascular fasciitis)
颅筋膜炎(Cranial fasciitis)
8828/0增生性筋膜炎(Proliferative fascitis)
8828/0 增生性肌炎(Proliferative myositis)
骨化性肌炎和指趾纤维骨性假瘤
(Myositis ossificans and fibro-osseous pseudotumour of digits)
缺血性筋膜炎(Ischaemic fasciitis)
8820/0弹力纤维瘤(Elastofibroma)
8992/0婴儿纤维性错构瘤(Fibrous hamartoma of infancy)
结肠纤维瘤病(Fibromatosis colli)
幼年性玻璃样变纤维瘤病(Juvenile hyaline fibromatosis)
包涵体纤维瘤病(Inclusion body fibromatosis)
8813/0 腱鞘纤维瘤(Fibroma of tendon sheath)
8810/0增生性纤维母细胞瘤(Desmoplastic fibroblastoma)
8825/0 肌纤维母细胞瘤(Myofibroblastoma)
8816/0钙化性腱膜纤维瘤(Calcifying aponeurotic fibroma)
EWSRI-SMAD3阳性纤维母细胞瘤(新增)
(EWSR1-SMAD3-positive fibroblastic tumour(emerging))
8826/0血管肌纤维母细胞瘤(Angiomyofibroblastoma)
9160/0 细胞性血管纤维瘤(Celular angiofibroma)
9160/0 血管纤维NOS (Angiofibroma NOS)
8810/0项型纤维瘤(Nuchal fibroma)
8811/0肢端纤维粘液瘤(Acral fibromyxoma)
8810/0 Gardner纤维瘤(Gardner fibroma)
中间性(局部侵袭性)Intermediate (locally aggressive)
8815/0 孤立性纤维性肿瘤,良性(Solitary fibrous tumour, benign)
8813/1掌跖纤维瘤病(Palmar/plantar-type fibromatosis)
8821/1韧带样纤维瘤病(Desmoid-type fibromatosis)
8821/1 腹外带样纤维瘤病(Extra-abdominal desmoid fibromatosis)
8822/1 腹部纤維瘤病(Abdominal fibromatosis)
8851/1 脂肪纤维瘤病(Lipofibromatosis)
8834/1巨细胞纤维母细胞瘤(Giant cell fibroblastoma)
中间性(偶有转移性)Intermediate(rarely metastasizing)
8832/1 隆突性皮肤纤维肉瘤NOS (Dermatofibrosarcoma protuberans NOS)
8833/1色索性隆突性皮肤纤维肉瘤(Pigmented dermatofibrosarcoma protuberans)
8832/3纤维肉瘤性隆突性皮肤纤维肉瘤
(Dermatofibrosarcoma protuberans, fibrosarcomatous)
黏液性隆突性皮肤纤維肉瘤
(Myxoid dermatofibrosarcoma protuberans)
隆突性皮肤纤维肉瘤伴肌样分化
(Dermatofibrosarcoma protuberans with myoid differentiation)
斑块样隆突性皮肤纤维肉瘤
(Plaque-like dermatofibrosarcoma protuberans)
8815/1孤立性纤维性肿瘤NOS (Solitary fibrous tumour NOS)
脂肪形成(脂防瘤性)孤立性纤维性肿瘤
(Fat-forming(lipomatous) solitary fibroustumour)
富巨細胞性孤立性纤維性肿瘤(Giant cell-rich solitary fibrous tumour)
8825/1炎性肌成纤维細胞性肿瘤(Inflammatory myofibroblastic tumour)
上皮样炎性肌纤维母细胞肉瘤
(Epithelioid inflammatory myofibroblastic sarcoma)
8825/3肌纤维母细胞肉瘤(Myofibroblastic sarcoma)
8810/1 CD34阳性浅表纤维母细胞瘤
(Superficial CD34-positive fibroblastic tumour)
8811/1 點液炎性纤维母细胞肉瘤(Myxoinflammatory fibroblastic sarcoma)
8814/3 婴儿纤维肉瘤(Infantile fibrosarcoma)
恶性(Malignant)
8815/3孤立性纤维性肿瘤,恶性(Solitary fibrous tumour, malignant)
8810/3维肉NOS (Fibrosarcoma NOS)
8811/3 黏液性纤维肉瘤(Myxofibrosarcoma)
上皮样點液性纤维肉瘤(Epithelioid myxofibrosarcoma)
8840/3低度恶性纤维黏液样肉瘤(Low-grade fibromyxoid sarcoma)
8840/3 硬化性上皮样纤维肉瘤(Sclerosing epithelioid fibrosarcoma)
所谓的纤维组织细胞性肿瘤(So-called fibrohistiocytic tumours)
良性(Benign)
9252/0 鞘鞘巨细胞肿瘤NOS (Tenosynovial giant cell tumour NOS)
9252/1 腱鞘巨细胞肿瘤，弥漫型(Tenosynovial giant cell tumour, diffuse)
8831/0 深部良性纤维組织细胞瘤(Deep benign fibrous histiocytoma)
中间性(偶有转移性)Intermediate(rarely metastasizing)
8835/1 丛状纤维组织细胞瘤(Plexiform fibrohistiocytic tumour)
9251/1 软组织巨细胞瘤(Giant cell tumour of soft parts NOS)
恶性(Malignant)
9252/3 恶性鞘巨细胞瘤(Malignant tenosynovial giant cell tumour)
血管性肿瘤(Vascular tumours)
良性(Benign)
9120/0 血管瘤NOS (Haemangioma NOS)
9132/0 肌内血管瘤(Intramuscular haemangioma)
9123/0 动静詠血管(Arteriovenous haemangioma)
9122/0 静脉型血管(Venous haemangioma)
9125/0上皮样血管瘤(Epithelioid haemangioma)
细胞性上皮样血管瘤(Cellular epithelioid haemangioma)
非典型上皮样血管瘤(Atypical epithelioid haemangioma)
9170/0淋巴管瘤NOS (Lymphangioma NOS)
淋巴管瘤病(Lymphangiomatosis)
9173/0 囊性淋巴管瘤(Cystic lymphangioma)
9161/0 获得性袢状血管瘤(Acquired tufted haemangioma)
中间性(局部侵装性)Intermediate (locally aggressive)
9130/1卡波西型血管内皮瘤(Kaposiform haemangioendothelioma)
中间性(偶有转移性)Intermediate(rarely metastasizing)
9136/1网状血管内皮瘤(Retiform haemangioendothelioma)
9135/1乳头状淋巴管内血管内皮瘤(Papillary intralymphatic angioendothelioma)
9136/1 混合性血管内皮瘤(Composite haemangioendothelioma)
神经内分泌性混合性血管内皮瘤
(Neuroendocrine composite haemangioendothelioma)
9140/3卡波西肉瘤(Kaposi sarcoma)
经典型情性卡波西肉瘤(Classic indolent Kaposi sarcoma)
非洲地方性卡波西肉瘤(Endemic African Kaposi sarcoma)
艾滋病相关性卡波西肉瘤(AIDS-associated Kaposi sarcoma)
迟发型卡波西肉瘤(latrogenic Kaposi sarcoma)
9138/1假性肌(类上皮肉瘤样)血管内皮细胞瘤
(Pseudomyogenic (epithelioidsarcoma-like)haemangioendothelioma)
恶性(Malignant)
9133/3 上皮样血管内皮瘤NOS
(Epithelioid haemangioendothelioma NOS)
上皮样血管内皮瘤伴WWTR1-CAMTA1融合
(Epithelioid haemangioendothelioma withWWTR1-CAMTA1 fusion)
上皮样血管内皮瘤伴YAP1-TFE3融合
(Epithelioid haemangioendothelioma withYAP1-TFE3 fusion)
9120/3 血管肉瘤(Angiosarcoma)
周细胞性(血管周细胞性)肿瘤(Pericytic(perivascular) tumours)
良性和中间性(Benign and intermediate)
8711/0 血管球瘤NOS (Glomus tumour NOS)
8712/0 血管球瘤(Glomangioma)
8713/0 血管球肌瘤(Glomangiomyoma)
8711/1 血管球瘤病(Glomangiomatosis)
8711/1 恶性潜能不确定性血管球肿瘤
(Glomus tumour of uncertain malignant potential)
8824/0肌周细胞瘤(Myopericytoma)
8824/1 肌纤维瘤病(Myofibromatosis)
8824/0肌纤维瘤(Myofibroma)
8824/1 婴儿性肌纤维瘤病(Infantile myofibromatosis)
8894/0血管平滑肌瘤(Angioleiomyoma)
恶性(Malignant)
8711/3恶性血管球(Glomus tumour, malignant)
骨肌肿瘤(Skeletal muscle tumours)
良性(Benign)
8900/0横纹肌NOS (Rhabdomyoma NOS)
8903/0 胎儿型横纹肌瘤(Fetal rhabdomyoma)
8904/0 成人型横纹肌瘤(Adult rhabdomyoma)
8905/0 生殖道型横纹肌瘤(Genital rhabdomyoma)
恶性(Malignant)
8910/3 胚胎性横纹肌肉瘤NOS (Embryonal rhabdomyosarcoma NOS)
8910/3 胚胎性横纹肌肉瘤,多形性(Embryonal rhabdomyosarcoma, pleomorphic)
8920/3 腺泡状横纹肌肉瘤(Alveolar rhabdomyosarcoma)
8901/3 多形性横纹肌肉NOS (Pleomorphic rhabdomyosarcoma NOS)
8912/3梭形细胞性横纹肌肉瘤(Spindle cell rhabdomyosarcoma)
先天性梭形细胞横纹肌肉瘤伴VGLL2/NCOA2/ CITED2重排
(Congenital spindle cellhabdomyosarcoma with VGLL2/NCOA2/CITED2 rearrangements)
MYOD1-突变梭形细胞性/硬化性横纹肌肉瘤
(MYOD1-mutant spindle cell/sclerosing rhabdomyosarcoma)
骨内梭状细胞横纹肌肉瘤(伴TFCP2/NCOA2重排)
(Intraosseous spindle cell rhabdomyosarcoma (with TFCP2/NCOA2 rearrangements))
8921/3 外胚层间叶瘤(Ectomesenchymoma)
胃肠道间质瘤(Gastrointestinal stromal tumours)
8936/3胃肠道间质瘤(Gastrointestinal stromal tumour)
软骨-骨性肿瘤(Chondro-osseous tumours)
良性(Benign)
9220/0 软骨瘤NOS (Chondroma NOS)
软骨母细胞瘤样软组织软骨瘤 (Chondroblastoma-like soft tissue chondroma)
恶性(Malignant)
9180/3 骨外骨肉瘤(Osteosarcoma, extraskeletal)
周围神经鞘肿瘤(Peripheral nerve sheath tumours)
良性(Benign)
9560/0 神经鞘瘤NOS (Schwannoma NOS)
9560/0 陈旧性神经鞘瘤(Ancient schwannoma)
9560/0 细胞性神经鞘瘤(Cellular schwannoma)
9560/0 丛状神经鞘(Plexiform schwannoma)
上皮样神经鞘瘤(Epithelioid schwannoma)
微囊/网状神经鞘瘤(Microcystic/reticular schwannoma)
9540/0 神经纤维瘤NOS (Neurofibroma NOS)
陈旧神经纤维瘤(Ancient neurofibroma)
细胞性神经纤维瘤(Cellular neurofibroma)
非典型神经纤维瘤(Atypical neurofibroma)
9550/0 丛状神经纤维瘤(Plexiform neurofibroma)
9571/0 神经束膜瘤NOS (Perineurioma NOS)
网状神经束膜瘤(Reticular perineurioma)
硬化性神经東膜瘤(Sclerosing perineurioma)
9580/0颗粒细胞瘤NOS (Granular cell tumour NOS)
9562/0 神经鞘黏液瘤(Nerve sheath myxoma)
9570/0孤立性局限性神经瘤(Solitary circumscribed neuroma)
丛状孤立性局限性神经瘤(Plexiform solitary circumscribed neuroma)
9530/0 脑膜NOS (Meningioma NOS)
良性蝾螈瘤/神经肌肉性迷芽瘤
(Benign triton tumour /neuromuscular choristoma)
9563/0 混杂性神经鞘瘤(Hybrid nerve sheath tumour)
神经束膜瘤/神经鞘瘤(Perineurioma/schwannoma)
神经鞘瘤/神经纤维瘤(Schwannoma/neurofibroma)
神经束膜瘤/神经纤维瘤(Perineurioma/neurofibroma)
恶性(Malignant)
9540/3恶性周神经鞘膜瘤NOS
(Malignant peripheral nerve sheath tumour NOS)
9542/3上皮样恶性周围神经鞘膜瘤
(Malignant peripheral nerve sheath tumour,epithelioid)
9540/3黑色素性恶性周围神经鞘膜瘤
(Melanotic malignant peripheral nerve sheathtumour)
9580/3恶性颗粒细胞瘤(Granular cell tumour, malignant)
9571/3 恶性神经鞘瘤(Perineurioma, malignant)
未确定分化的肿瘤(Tumours of uncertain differentiation)
良性(Benign)
8840/0 黏液瘤NOS (Myxoma NOS)
细胞性黏液瘤(Cellar myxoma)
8841/0 侵袭性血管黏液瘤(Aggressive angiomyxoma)
8802/1 多形性透明变性血管扩张性肿瘤
(Pleomorphic hyalinizing angiectatic tumour)
8990/0 磷酸盐尿性间叶性肿瘤NOS
(Phosphaturic mesenchymal tumour NOS)
8714/0 良性血管周围上皮样瘤(Perivascular epithelioid tumour, benign)
8860/0血管平滑肌脂肪瘤(Angiomyolipoma)
中间性(局部侵袭性)Intermediate (locally aggressive)
8811/1 含铁血黄素沉着性纤维脂肪瘤性肿瘤
(Haemosiderotic fibrolipomatous tumour)
8860/1 上皮样血管平滑肌脂肪瘤(Angiomyolipoma, epithelioid)
中间性(偶有转移性)Intermediate(rarely metastasizing)
8830/1 非典型纤维黄色瘤(Atypical fibroxanthoma)
8836/1 血管瘤样纤维组织细胞瘤(Angiomatoid fibrous histiocytoma)
8842/0 骨化性纤维黏液样瘤(Ossifying fibromyxoid tumour NOS)
8940/0 混合NOS (Mixed tumour NOS)
8940/3 性混合NOS (Mixed tumour, malignant,NOS)
8982/0 肌上皮瘤NOS (Myoepithelioma NOS)
恶性(Malignant)
8990/3恶性磷酸盐尿性间叶性肿瘤
(Phosphaturic mesenchymal tumour, malignant)
NTRK重排的梭形细胞肿瘤(新出现)
(NTRK-rearranged spindle cell neoplasm(emerging))
9040/3 滑膜肉NOS (Synovial sarcoma NOS)
9041/3 滑膜肉瘤，梭形细胞型(Synovial sarcoma, spindle cell)
9043/3 滑膜肉瘤，双相型(Synovial sarcoma, biphasic)
滑膜肉瘤，低分化型(Synovial sarcoma, poorly differentiated)
8804/3上皮样肉瘤(Epithelioid sarcoma)
近端或大细胞型上皮样肉瘤(Proximal or large cell epithelioid sarcoma)
典型样上皮样肉瘤(Classic epithelioid sarcoma)
9581/3 腺泡状软组织肉瘤(Alveolar soft part sarcoma)
9044/3软组织透明细胞肉瘤(Clear cell sarcoma NOS)
9231/3 骨外黏液样软骨肉瘤(Extraskeletal myxoid chondrosarcoma)
8806/3促结缔组织增生性小圆细胞肿瘤(Desmoplastic small round cell tumour)
8963/3 横纹肌样瘤(Rhabdoid tumour NOS)
8714/3 恶性血管周围上皮样肿瘤(Perivascular epithelioid tumour, malignant)
9137/3血管内膜肉瘤(Intimal sarcoma)
8842/3骨化性纤维黏液样肿瘤，恶性
(Ossifying fibromyxoid tumour, malignant)
8982/3 肌上皮癌(Myoepithelial carcinoma)
8805/3 未分化肉瘤(Undifferentiated sarcoma)
8801/3梭形细胞肉瘤，未分化 (Spindle cell sarcoma, undifferentiated)
8802/3多形性肉瘤，未分化(Pleomorphic sarcoma, undifferentiated)
8803/3圆形细胞肉瘤，未分化(Round cell sarcoma, undifferentiated)
